福島県立医科大学学術成果リポジトリ = Fukushima Medical University Repository >
福島医学会 = The Fukushima Society of Medical Science >
Fukushima Journal of Medical Science >
Vol.60 (2014) >
このアイテムの引用には次の識別子を使用してください:
http://ir.fmu.ac.jp/dspace/handle/123456789/434
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タイトル: | A case of a child with sle presenting with hps as a primary manifestation |
著者: | Ono, Atsushi Kawasaki, Yukihiko Kanno, Syuto Ohara, Shinichiro Sakai, Nobuko Suyama, Kazuhide Hosoya, Mitsuaki |
学内所属: | 小児科学講座 |
誌名/書名: | Fukushima Journal of Medical Science |
巻: | 60 |
号: | 2 |
開始ページ: | 181 |
終了ページ: | 186 |
発行日: | 2014年 |
抄録: | The primary manifestations of systemic lupus erythematosus (SLE) are various. One such manifestation is hemophagocytic syndrome (HPS). We here report a child with SLE presenting with HPS as a primary manifestation. In October 2010, an 11-year-old Japanese boy presented with pancytopenia, elevated liver enzymes, hyperferritinemia and hemophagocytosis due to macrophages in the bone marrow, and was diagnosed with HPS. A year later, he was found to have proteinuria and hematuria. Oral aphtha and Raynaud's phenomenon were observed, and the patient showed low serum complement levels and was positive for anti-nuclear antibodies (ANAs). He was subsequently diagnosed with SLE. Moreover, low serum complement levels and ANA positivity were detected in a serum sample preserved at the onset of HPS. The HPS was considered to be a primary manifestation of SLE on the basis of these findings. Based on this case, the presence of an underlying disease, such as SLE, should be investigated in cases of HPS. |
出版者: | The Fukushima Society of Medical Science |
出版者(異表記): | 福島医学会 |
本文の言語: | eng |
このページのURI: | http://ir.fmu.ac.jp/dspace/handle/123456789/434 |
本文URL: | http://ir.fmu.ac.jp/dspace/bitstream/123456789/434/1/FksmJMedSci_60_p181.pdf |
ISSN: | 0016-2590 2185-4610 |
DOI: | 10.5387/fms.2013-24 |
PubMed番号: | 25747608 |
関連ページ: | http://doi.org/10.5387/fms.2013-24 |
権利情報: | © 2014 The Fukushima Society of Medical Science |
出現コレクション: | Vol.60 (2014)
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