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Vol.60 (2014) >

Please use this identifier to cite or link to this item: http://ir.fmu.ac.jp/dspace/handle/123456789/434

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Title: A case of a child with sle presenting with hps as a primary manifestation
Authors: Ono, Atsushi
Kawasaki, Yukihiko
Kanno, Syuto
Ohara, Shinichiro
Sakai, Nobuko
Suyama, Kazuhide
Hosoya, Mitsuaki
Affiliation: 小児科学講座
Source title: Fukushima Journal of Medical Science
Volume: 60
Issue: 2
Start page: 181
End page: 186
Issue Date: 2014
Abstract: The primary manifestations of systemic lupus erythematosus (SLE) are various. One such manifestation is hemophagocytic syndrome (HPS). We here report a child with SLE presenting with HPS as a primary manifestation. In October 2010, an 11-year-old Japanese boy presented with pancytopenia, elevated liver enzymes, hyperferritinemia and hemophagocytosis due to macrophages in the bone marrow, and was diagnosed with HPS. A year later, he was found to have proteinuria and hematuria. Oral aphtha and Raynaud's phenomenon were observed, and the patient showed low serum complement levels and was positive for anti-nuclear antibodies (ANAs). He was subsequently diagnosed with SLE. Moreover, low serum complement levels and ANA positivity were detected in a serum sample preserved at the onset of HPS. The HPS was considered to be a primary manifestation of SLE on the basis of these findings. Based on this case, the presence of an underlying disease, such as SLE, should be investigated in cases of HPS.
Publisher: The Fukushima Society of Medical Science
Publisher (Alternative foam): 福島医学会
language: eng
URI: http://ir.fmu.ac.jp/dspace/handle/123456789/434
Full text URL: http://ir.fmu.ac.jp/dspace/bitstream/123456789/434/1/FksmJMedSci_60_p181.pdf
ISSN: 0016-2590
2185-4610
DOI: 10.5387/fms.2013-24
PubMed ID: 25747608
Related Page: http://doi.org/10.5387/fms.2013-24
Rights: © 2014 The Fukushima Society of Medical Science
Appears in Collections:Vol.60 (2014)

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FksmJMedSci_60_p181.pdf750.85 kBAdobe PDFDownload

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